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Old 09-09-2012
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Arrow Gyrus Daily Questions; Pediatrics #31

Large dose of pyridoxine are of value in some cases of ?

A) Phenylketonuria.
B) Homocystinuria.
C) NonKetotic hyperglycemia.
D) Ketotic hypoglycemia
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Old 09-09-2012
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C ) homocytinuria , some cases respond to High B6
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B....cystathionine synthase deficiency....sometimes responds to mega doses of B6 treatment
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Old 09-09-2012
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Oh i see i said wrong option i wanted to say B ) homocystinuria wrote C instead
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No specific cure has been discovered for homocystinuria; however, many people are treated using high doses of vitamin B6 (also known as pyridoxine).[4] Slightly less than 50% respond to this treatment and need to intake supplemental vitamin B6 for the rest of their lives. Those who do not respond require a low methionine diet, and most will need treatment with trimethylglycine. A normal dose of folic acid supplement and occasionally adding cysteine to the diet can be helpful.
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Answer is B Homocystinuria..

Pridoxin is used in Rx for many conditions..

Homocystinuria,cystathionuria,oxaluria and Neonatal seizures (Pyridoxin responsive Seizures)
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Old 09-10-2012
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Other Vit depentent conditions


Niacin is used in treatment of Harnup disease.
Cynacobalamin -- Methy malonic acidemia and megalablastic anaemia.

Biotin - Propionic acidemia.

Vit C - For chediak higashi...

Last edited by cingulate.gyrus; 09-10-2012 at 05:04 AM. Reason: add
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