MNEMONIC for Glycogen Storage Diseases:
Very Poor Casing And Metabolism of Hers
Note: casing refers to storage
POMPe's trashes the PUMP (cardiomegaly)
HERS Disease- its HEpatic glycogen phosphorylase deficiency
McArdles- its Muscle Glycogen phosphorylase deficiency
Very Poor Casing And Metabolism of Hers
Note: casing refers to storage
- I- Von Gierke's (Glu6P deficiency)
- II- Pompe's (lysosmal 1,4 glucosidase)
- III- Cori (1,6 glucosidase)
- IV- Anderson (glycogen branching enzyme)
- V- McArdles (Muscle GlycogenPhosphoylase )
- VI- Hers disease (Hepatic Glycogen Phosphorylase)
POMPe's trashes the PUMP (cardiomegaly)
HERS Disease- its HEpatic glycogen phosphorylase deficiency
McArdles- its Muscle Glycogen phosphorylase deficiency